Diagnosis of congenital long QT interval syndrome in a 16-year old girl
https://doi.org/10.51523/2708-6011.2021-18-2-18
Abstract
The article presents a clinical case of a 16-year-old girl with clinical manifestations of congenital long QT interval syndrome in the form of syncope which were primarily diagnosed as epileptic syndrome for which the patient was taking anticonvulsant drugs having qualities of secondary prolongation of QT interval. At the same time, the data of family anamnesis (sudden death of the mother at a young age) in combination with typical manifestations of disease and electrocardiographic signs (prolonged QT interval measured from the standard electrocardiogram, paroxysms of spindle-shaped ventricular tachycardia accompanied with syncope conditions) made it possible to diagnose congenital long QT interval syndrome and implant an electric cardiac pacemaker.
About the Authors
N. A. Skuratova
Gomel State Medical University; Gomel Regional Children’s Clinical Hospital
Belarus
Belarus
Natalia A. Skuratova, PhD (Med), Associate Professor at the Department of Pediatrics
Gomel
A. I. Zaryankina
Gomel State Medical University
Belarus
Belarus
Alla I. Zaryankina, PhD (Med), Associate Professor, Head of the Department of Pediatrics
Gomel
A. A. Kozlovsky
Gomel State Medical University
Belarus
Belarus
Alexandr A. Kozlovsky, PhD (Med), Associate Professor at the Department of Pediatrics
Gomel
S. S. Ivkina
Gomel State Medical University
Belarus
Belarus
Svetlana S. Ivkina, PhD (Med), Associate Professor at the Department of Pediatrics
Gomel
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Review
For citations:
Skuratova N.A., Zaryankina A.I., Kozlovsky A.A., Ivkina S.S. Diagnosis of congenital long QT interval syndrome in a 16-year old girl. Health and Ecology Issues. 2021;18(2):126-130. (In Russ.) https://doi.org/10.51523/2708-6011.2021-18-2-18
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