zdorПроблемы здоровья и экологииHealth and Ecology Issues2220-09672708-6011Gomel State Medical University10.51523/2708-6011.2011-8-2-7zdor-1091Research ArticleКЛИНИЧЕСКАЯ МЕДИЦИНАCLINICAL MEDICINEНАСЛЕДСТВЕННЫЙ СФЕРОЦИТОЗ У ДЕТЕЙ: СОВРЕМЕННЫЕ ПРЕДСТАВЛЕНИЯ (обзор литературы)HEREDITARY SPHEROCYTOSIS IN CHILDREN: MODERN CONCEPTION (literature review)МицураЕ. Ф.MitsuraE. F.noemail@neicon.ruРеспубликанский научно-практический центр радиационной медицины и экологии человекаRepublican Research Centre for Radiation Medicine and Human Ecology201128062011023944Copyright © Мицура Е.Ф., 20112011Мицура Е.Ф.Mitsura E.F.Данная работа распространяется под лицензией Creative Commons Attribution 4.0.This work is licensed under a Creative Commons Attribution 4.0 License.https://journal.gsmu.by/jour/article/view/1091

В статье рассмотрены основные взгляды на наследственный сфероцитоз - распространенное наследственное заболевание, проявляющееся гемолитической анемией, желтухой и спленомегалией. Приводится классификация наследственного сфероцитоза, подходы к диагностике и лечению в зависимости от тяжести течения заболевания и наличия наиболее частых осложнений.

The modern conception of hereditary spherocytosis has been considered in the article. Hereditary spherocytosis is a common inherited disease declaring itself in haemolytic anaemia, jaundice and splenomegaly. The contemporary classification, approaches to the diagnosis and treatment depending on severity of the disease course and presence of the most frequent complications have been given.

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The authors declare that there are no conflicts of interest present.